Sjögren Syndrome. Two cases report

Authors

  • Maira Verena Guerrero Aguilar Hospital Universitario Carlos Manuel de Céspedes. Bayamo. Granma.
  • José Miguel Acosta García Hospital Universitario “Carlos Manuel de Céspedes. Bayamo. Granma.
  • Lidia Rosa Cutiño Montero Hospital Universitario “Carlos Manuel de Céspedes. Bayamo. Granma.
  • Luis Augusto Pompa Milanés Hospital Universitario “Carlos Manuel de Céspedes. Bayamo. Granma.

Abstract

Introduction: the Sjögren syndrome is an autoimmune disease; this means that the immune system attacks its own cells. The immune system attacks the glands that produce secretions and humidity causing dryness in the mouth and in the eyes, other parts of the body can be affected causing a variety of possible symptoms.
Case presentation
: it was presented a 12 year- old- masculine patient, of rural origin (Jiguaní), white race, with 4 month antecedents before the hospitalization with a volume increase in the right pre auricular region, with eye dryness symptoms and little saliva, who was hospitalized on April 12, 2010, to be surgically treated on April 13, and a 22 feminine patient of rural origin with repeated antecedents of parotitis, keratoconjunctivitis, dry mouth and occasional articular pains, with a facial paralysis; remaining like a sequel the paralysis of the inferior facial branch. Both patients presented a Primary and Secondary Syndrome of Sjögren.
Discussion
: recently it has been recognized an entity, similar to the SS: the syndrome of infiltrating diffuse Lymphocytosis (SIDL), but is affects preferably to masculine patients infected with the HIV, the lymphocytes participants are of type CD8, instead of CD4 as it occurs in the SS.
Conclusions
: both patients were surgically treated and they keep their treatments with the Otolaryngology, Ophthalmology and Rheumatology services. According to the symptoms of the patients and the physical examination, the child was considered a Primary Sjogren Syndrome (PSS) and to the youngster was considered a Secondary Sjogren Syndrome (SSS).

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Author Biographies

Maira Verena Guerrero Aguilar, Hospital Universitario Carlos Manuel de Céspedes. Bayamo. Granma.

Especialista de Primer Grado en Otorrinolaringología. Máster en Enfermedades Infecciosas. Asistente.

José Miguel Acosta García, Hospital Universitario “Carlos Manuel de Céspedes. Bayamo. Granma.

Especialista de Primer Grado en Otorrinolaringología. Asistente.

Lidia Rosa Cutiño Montero, Hospital Universitario “Carlos Manuel de Céspedes. Bayamo. Granma.

Especialista de Primer Grado en Otorrinolaringología. Asistente.

Luis Augusto Pompa Milanés, Hospital Universitario “Carlos Manuel de Céspedes. Bayamo. Granma.

Especialista de Primer Grado en Otorrinolaringología. Asistente.

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Published

2014-07-01

How to Cite

1.
Guerrero Aguilar MV, Acosta García JM, Cutiño Montero LR, Pompa Milanés LA. Sjögren Syndrome. Two cases report. RM [Internet]. 2014 Jul. 1 [cited 2025 May 21];18(3). Available from: https://revmultimed.sld.cu/index.php/mtm/article/view/70

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